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Description
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Aplican condiciones

Stroke 37:524530 Roe CR, Millington DS, Maltby DA, Bohan TP, Hoppel CL (1984) l-Carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia

Secondary hyperammonemia 2/2 disorders that inhibit the urea cycle : ATP-deficiency (results in CPS1 deficiency) Valproate metabolism
